Title

Opsoclonus-myoclonus with Beckwith-Wiedemann syndrome and hepatoblastoma

Author

Wilfong AA; Parke JT; McCrary JA 3d

Address

Department of Pediatric Neurology, Baylor College of Medicine, Texas Children's Hospital, Houston 77030

Source

Pediatr Neurol, 8(1):77-9 1992 Jan-Feb

Abstract

The association between Beckwith-Wiedemann syndrome and hepatoblastoma is well established and relatively commonplace. The occurrence of opsoclonus-myoclonus syndrome in individuals with occult neoplasia is also well documented. However, the development of opsoclonus-myoclonus syndrome in an infant with Beckwith-Wiedemann syndrome and hepatoblastoma has not been reported previously. The list of underlying causes of opsoclonus-myoclonus syndrome should be expanded to include hepatoblastoma, particularly in any child with features suggestive of Beckwith-Wiedemann syndrome.

Language

English

Unique Identifier

92215299

MESH Headings

Beckwith-Wiedemann Syndrome *DI ; Biopsy ; Carcinoma, Hepatocellular *DI ; Case Report ; Diagnosis, Differential ; Epilepsy, Myoclonic *DI ; Female ; Human ; Infant ; Liver PA ; Liver Neoplasms *DI ; Neurologic Examination ; Ocular Motility Disorders *DI ; Paraneoplastic Syndromes *DI ; Tomography, X-Ray Computed

Publication Type

JOURNAL  ARTICLE

ISSN

0887-8994

Country of Publication

UNITED STATES